左颞部婴儿型纤维肉瘤1例报道并文献复习

Case report and literature review:a patient with infantile fibrosarcoma on left temple

目的了解婴儿型纤维肉瘤(IFS)的临床特点、病理、诊断、治疗及预后。方法对2015年12月我科病房收治的1例左颞部婴儿型纤维肉瘤病例进行回顾性分析,观察患儿进行规范化治疗后的症状、体征、实验室指标的变化,并进行文献复习。结果经6周期规范化疗后,患儿原发部位稳定,无复发,远处无转移,随诊无肿瘤复发。结论婴儿型纤维肉瘤是一种相对少见的、仅发生于婴幼儿的一类软组织肉瘤,缺乏特异性,最终需病理确诊;术后化疗可有效控制病情,防止复发。

Objective To investigate the clinical characteristics,pathological features,diagnosis,treatment and prognosis of infantile fibrosarcoma（congenital fibrosarcom,IFS）.Methods One case of infantile fibrosarcoma treated in Beijing Tongren Hospital in December 2015 was studied retrospectively.The signs,symptoms,laboratory values after standard chemotherapy was analyzed.Results After six cycles of standard chemotherapy,the primary location was stable,without recurrences and metastases,and no recurrences in late follow-up.Conclusions Infantile fibrosarcoma was a rare soft-tissue sarcoma that was occurred in infants and young children.The diagnosis was confirmed by pathologic examination because of specificity absence.The condition could be under control and no recurrences after standard postoperative chemotherapy.