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长期小剂量奎尼丁在Brugada综合征患者植入型心律转复除颤器应用一例 被引量:1

Effect of long-term low doses of quinidine in a patient with Brugada syndrome after implantable cardioverter defibrillator implantation
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摘要 Brugada综合征是由于编码心肌离子通道基因突变引起离子通道功能异常而导致的综合征.临床上,该综合征以V1~V3导联ST段抬高且多变、心脏结构无异常、多形性室性心动过速(室速)或心室颤动(室颤)和晕厥的反复发作,以及心脏性猝死为特征¨].植入型心律转复除颤器(ICD)植入术已成为治疗Brugada综合征有效的方法,但对于术后反复室性心律失常电风暴治疗手段有限,本文报道ICD植入联合长期小剂量奎尼丁治疗Brugada综合征伴反复室颤发作1例.
出处 《中华心律失常学杂志》 2016年第5期442-443,共2页 Chinese Journal of Cardiac Arrhythmias
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