肝脏恶性上皮样血管内皮瘤超声表现

Ultrasonographic manifestation of malignant epithelioid hemangioendothelioma in liver

目的分析肝上皮样血管内皮瘤(HEHE)的临床资料及影像学特点。方法报道首都医科大学宣武医院1例HEHE患者,回顾性分析其临床及影像学资料,并结合文献进行分析。结果 HEHE为肝脏罕见原发性血管性肿瘤,临床症状缺乏特异性。超声表现为散在类圆形高回声,形态规则,边界清晰,该例患者同时伴有双下肺多发结节影,临床确诊主要依据病理学诊断,HE染色中可见上皮样血管内皮细胞。结论HEHE是一种少见的低度恶性肿瘤,易误诊,影像学结合临床特点有助于提示其诊断,病理及免疫组化是其诊断金标准。

Objective To expore the clinical characteristics and imaging features of hepatic epithelioid hemangioendothclioma （HEHE）. Methods The clinical and imaging characteristics of one patients with HEHE in Xuanwu Hospital of Capital Medical University were retrospectively analyzed and the literature were reviewed. Results HEHE was a rare primary vascular tumor of the liver, with lack of specificity in clinical symptoms. Ultrasound showed diffuse hyperechoic, morphological rules and clear boundary. The patient was accompanied by multiple nodules of the lower lung. The diagnosis was based on pathological diagnosis. The epithelium endothelial cells were seen in HE staining. Conclusion HEHE is a rare low grade malignant tumor. It is easy to be misdiagnosed. The clinical features of HEHE combined with radiography are helpful to the diagnosis. Pathology and immunohistochemistry are the gold standard of diagnosis.