巴德-吉亚利综合征误诊1例报道

Misdiagnosis of Budd-Chiari syndrome:one case report

巴德-吉亚利综合征(Budd-Chiari syndrome,BCS)简称布加综合征,属临床少见病,多因其引起的门脉高压症而易误诊为隐源性肝硬化。临床典型表现为肝大、门-体侧支循环和腹水三联征。现将兰州军区兰州总医院近期收治1例初诊时误诊为隐源性肝硬化失代偿期的BCS患者报道如下,通过对该病例诊治过程的分析讨论,以期提高临床医师对该病的重视,减少临床误诊、误治。

Budd-Chiari syndrome （BCS） or syndrome de Budd-Chiari is a rare clinical disease, more because of the cause of portal hypertension, it is easily misdiagnosed as cryptogenic cirrhosis. Typical clinical manifestations are big liver, portac-aval collateral circulation and ascites. Now, one case of BCS was reported which misdiagnosed as crypto- genic decompensated cirrhosis. Based on the analysis of the process of diagnosis and treatment of the case discussion, in order to improve the clinical doctor＇ s emphasis on the disease, reduce misdiagnosis and mistherapy.