期刊文献+

重症肌无力伴视神经脊髓炎的临床特点及发病机制探讨(附二例报道) 被引量:2

Characteristic and pathogenesis of two patients with myasthenia gravis associated with neuromyelitis optica
原文传递
导出
摘要 重症肌无力(myasthenia gravis,MG)是最常见的神经肌肉接头疾病,以随意肌的波动性肌无力和易疲劳为特点。病变主要累及神经肌肉接头突触后膜上乙酰胆碱受体(AChR),是AChR抗体介导的、细胞免疫依赖性及补体参与的神经肌肉接头传递障碍的自身免疫性疾病。
出处 《中华神经医学杂志》 CAS CSCD 北大核心 2017年第1期82-85,共4页 Chinese Journal of Neuromedicine
关键词 重症肌无力 视神经脊髓炎 抗水通道蛋白-4抗体 发病机制 Myasthenia gravis Neuromyelitis optica Anti-aquaporin-4 antibody Pathogenesis
  • 相关文献

参考文献2

二级参考文献55

  • 1李翔,卢家红,乔健,肖保国,吕传真.重症肌无力患者外周血CD_4^+CD_(25)^(high)T细胞及其动态观察[J].中华神经科杂志,2006,39(11):766-770. 被引量:6
  • 2Lucchinetti CF,Mandler RN,McGavern D,et al.A role for humoral mechanisms in the pathogenesis of Devic's neuromyelitis optica[J].Brain,2002,125:1450-1461.
  • 3Mander RN.Neuromyelitis optica-Devic's syndrome,update[J].Autoimmun Rev,2006,5:537-543.
  • 4Fazekas F,Offenbacher H,Schmidt R,et al.MRI of neuromyelitis optica:evidence for a distinct entity[J].J Neurol Neurosurg Psychiatry,1994,57:1140-1142.
  • 5Bergamaschi R,Tonietti S,Franciotta D,et al.Oligoclonal bands in Devic's neuromyelitis optica and multiple sclerosis:differences in repeated cerebrospinal fluid examinations[J].Mult Scler,2004,10:2-4.
  • 6Lucchinetti CF,Parisi J,Bruck W.The pathology of multiple sclerosis[J].Neurol Clin,2005,23:77-105.
  • 7Lennon VA,Lucchinetti CF,Weinshenker BG.Identification of a marker autoantibody of neuromyelitis optica[J].Neurology,2003,60:A519.
  • 8Lennon VA,Wingerchuk DM,Kryzer TJ,et al.A serum autoantibody marker of neuromyelitis optica:distinction from multiple sclerosis[J].Lancet,2004,364:2106-2112.
  • 9Lennon VA,Kryzer TJ,Pittock SJ,et al.IgG marker of optic-spinal multiple sclerosis binds to the aquaporin-4 water channel[J].J Exp Med,2005,202:473-477.
  • 10Cunha FM,Scola RH,Werneck LC.Myasthenia gravis.clinical evaluation of 153 patients[J].Arq Neuropsiquiatr,1999,57:457-464.

共引文献4

同被引文献3

引证文献2

二级引证文献2

相关作者

内容加载中请稍等...

相关机构

内容加载中请稍等...

相关主题

内容加载中请稍等...

浏览历史

内容加载中请稍等...
;
使用帮助 返回顶部