韧带样型纤维瘤的MRI表现及病理对照分析

MRI Imaging Findings of Desmoid-Type Fibromatoses： Comparison with Pathological Results

目的探讨韧带样型纤维瘤（desmoid-type fibromatoses，DF）的MRJ表现及病理学特征。方法搜集19例行MRj检查的经手术与病理证实的DF病例，分析其MRJ特征与病理表现。结果腹外型18例，腹内型1例；肿瘤最大径平均8．5cm，19例均沿肌肉间隙生长，MRI平扫，T1WI呈等信号，信号轻度不均匀；T2WI呈明显不均匀高信号；15例行动态增强扫描，呈明显不均一强化、渐进性强化模式，其中13例瘤体内可见斑点状低信号区域。3例行DWI扫描，瘤体呈高信号。结论MRI可清晰显示瘤体形态及周围关系组织侵犯关系，瘤体内出现斑点状低信号、肿瘤沿肌间隙生长是DF的特征性MRI表现，MRI对DF手术范围的确定及治疗方案的确定具有重要的意义。

Objective To explore the MRI findings and pathologic features of desmoid type fibromatoses （DF）. Methods A total of 19 patients with DF confirmed by pathological and results were analyzed with imaging appearance and pathological characteristics. Results 18 cases located in extra-abdominal, 1 case located in intra- abdominal, the average tumor size is 8.5 cm. 19 cases all arose at the muscle spaces or along it. The tumors were iso-signal and heterogeneous signal on T1WI, On T2WI, the tumor appeared as heterogeneous high signal. 15 cases were scanned by dynamic contrast. 15 cases demonstrated obviously uneven enhancement on MRI after contrast and further strengthening on venous phase. Curvilinear areas of hypointensity were showed in 13 cases on both T1WI and T2WI images. On DWI, 3 cases showed higher signal. Conclusion MRI can clearly show around tumors form and organization infringement relations, tumors in the mottled low signal, along the muscle interstitial tumor growth is characteristic MRI manifestation of DF, MRI to determine the scope of DF surgery and treatment has the vital significance.