家族遗传性玻璃体变性混浊十例

Hereditary vitreous degeneration muddy:report of ten cases

家族遗传性玻璃体变性混浊临床较为罕见。本文报道两组家族遗传性玻璃体变性患者10例（13只眼），患眼玻璃体均呈白色致密棉絮状混浊或血性凝胶状混浊、质韧，且与视网膜粘连紧密，其中2例患者继发增殖性视网膜脱离。变性玻璃体HE染色呈红色无定形物质，甲基紫染色呈紫色。采用微创行玻璃体切割术，术前及术后辅以眼清合剂中药煎服治疗，疗效较好。

Hereditary vitreous degeneration muddy is rare in clinic. Here we report ten cases （thirteen eyes） of hereditary vitreous degeneration muddy from two families. All patients presented with vitreous opacity, and the textures appeared tough and tensile. Two cases had concurrent detachment of rhegmatogenous retina. HE staining showed red changeableness, and methyl violet staining appeared purple. All patients received vitrectomy with traditional Chinese medicine treatment, and got satisfactory efficacy.