遗传性血管性水肿的诊断及其鉴别

Diagnosis and identification of hereditary angioedema

血管性水肿作为一种临床症状,因常伴发风团疹而被诊断为荨麻疹。但对于不伴有风团的血管性水肿,目前应视为一种独立的疾病。引起血管水肿的原因,大体上可分为遗传性和获得性,而遗传性血管水肿因其发病率不高,尽管临床症状较重,甚至危及生命,但却常被误诊误治。因此非常有必要了解遗传性血管水肿的相关知识,提高对遗传性血管水肿的认知度。

Agioedema,as a clinical symptom,is often combined with wheals and diagnosed as urticaria. As to angioedema without wheals,it is considered an independent disease. According to the causes,angioedema is divided into 2 types：hereditary angioedema and acquired angioedema. As a rare disease,hereditary angioedema is often misdiagnosed and mistreated,although it is severe and life-threatening sometimes. It is therefore necessary to introduce how to identify and treat hereditary angioededa patients.