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胆道闭锁的病因新进展 被引量:3

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摘要 胆道闭锁是一种在儿童中由于纤维炎性组织堵塞肝内、外胆管最终导致肝衰竭的疾病。它是胆汁淤积症的最常见病因并且是在全世界范围内儿科学中进行肝移植的最常见指征,在儿童进行肝移植中占40%-50%。它是新生儿中进展最快的胆道疾病,在就诊时肝外胆管已经完全闭锁。如果不进行治疗,进行性肝纤维化将会导致肝硬化、门脉高压、肝衰竭,最终导致在2岁左右死亡。
出处 《新疆医学》 2017年第1期84-88,共5页 Xinjiang Medical Journal
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