盆腔炎性肌纤维母细胞瘤1例报告并文献复习

A Case Report on a Child with Pelvic Inflammatory Myofibroblastic Tumor

目的探讨盆腔炎性纤维母细胞瘤(IMT)的临床表现、影像学检查、病理学特性及诊断方法和预后。方法报道1例盆腔IMT患儿的临床资料,并复习国内外相关文献,分析和总结IMT的病因、发病部位、症状、影像学检测、诊治方法、病理学检测(包括免疫组化)和远期预后。结论 IMT是一种罕见疾病,好发于青少年及儿童,其发病年龄、发病位置、临床表现、影像学检查无特征性;其良恶性仍存在争议,具有潜在恶性,可复发、可转移;手术切除为目前唯一有效的治疗方法。

Objective To investigate the clinical manifestation, iconography detection, pathology character, diagnostic method and prognosis of inflammatory myofibroblastic tumor （IMT）. Methods The clinical data such as cause, site, symptom, iconography detection, treatment, pathologic detection （immunohistochemisty） and long-term prognosis of IMT of a child with inflammatory myofibroblastic tumor in cavitas pelvis was collected and analyzed by reviewing the domestic and abroad pertinent literatures. Conclusion IMT is a rare disease which is more likely to happen in children and teenagers. There were no characteristic manifestations in age of onset, position of onset, clini- cal features and iconography detection. It remains controversial on whether it is virtuous, malignancy or hidden malignancy. It may recur- rence or metastasize. Surgical resection is the only effective method to treat the disease so far.