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肺淋巴管肌瘤病并双肾、腹膜后多发血管平滑肌脂肪瘤一例 被引量:1

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摘要 肺淋巴管肌瘤病(pulmonary lymphangioleiomyomatosis,PLAM)是一种相对罕见、病因不明、持续发展的弥漫性肺间质疾病。散发的LAM发病率大约为总人口的百万分之一,但在遗传性疾病结节性硬化症(tuberous sclerosis complex,TSC)的女性患者中,PLAM的发病率很高(26%~39%)[1]。
出处 《海南医学》 CAS 2017年第11期1878-1880,共3页 Hainan Medical Journal
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  • 1Johnson SR. Lymphangioleiomyomatosis. Eur Respir J, 2006,27: 1056-1065.
  • 2Crino PB, Nathanson KL, Henske EP. The tuberous sclerosis complex. N Engl J Med, 2006, 355 : 1345-1356.
  • 3Ryu JH, Moss J, Beck G J, et al. The NHLBI lymphangioleiomyomatosis registry. Characteristcs of 230 patients at enrollment. Am J Respir Crit Care Med, 2006, 173: 105-111.
  • 4Young LR, Inoue Y, McCormack FX. Diagnostic Potential of serum VEGF-D for lymphangioleiomyomatosis. N Engl J Med, 2008, 358: 199-200.
  • 5Crooks DM, Pacheco-Rodriguez G, DeCastro RM, et al. Molecular and genetic analysis of disseminated neoplastic cells in lymphangioleiomyomatosis. Proc Natl Acad Sci USA, 2004, 101: 17462-17467.
  • 6Schiavina M, Contini P, Fabiani A, et al. Efficacy of hormonal manipulation in lymphangioleiomyomatosis. A 20-year-experience in 36 patients. Sarcoidosis Vasc Diffuse Lung Dis, 2007, 24 : 39- 50.
  • 7Taveira-DaSilva AM, Stylianou MP, Hedin C J, et al. Decline in lung function in patients with lymphangioleiomyomatosis treated with or without progesterone. Chest, 2004, 126 : 1867-1874.
  • 8Harari S, Cassandro R, Chiodini J, et al. Effects of a gonadotrophin-releasing hormone analogue on lung function in lymphangioleiomyomatosis. Chest, 2008, 133:448-454.
  • 9Juvet SC, McConnack FX, Kwiatkowski DJ, et al. Molecular pathogenesis of lymphangioleiomyomatosis. Lessons learned from orphans. Am J Respir Cell Mol Biol, 2007, 36: 398-408.
  • 10Bissler JJ, McCormack FX, Young LR, et al. Sirolimus for angiomyolipoma in tuberous sclerosis complex or lymphangioleiomyomatosis. N Engl J Med, 2008, 358: 140-151.

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