小儿胰腺实性假乳头状瘤四例临床分析

Pancreatic solid pseudopapillary neoplasm in pediatric patients： report of 4 cases

回顾性分析2000年1月至2016年1月诊治的4例胰腺实性假乳头状瘤（SPN）患儿的临床资料。4例均为女性，年龄8～13岁。临床表现3例为无意中发现腹部包块、1例间断性腹痛而行腹部超声检查时发现胰腺肿物就诊，经过相关实验室及影像学检，成功行手术切除，病理检查结果诊断，病变位于胰体尾部。术后患儿顺利恢复，最长随访时间6．0年无复发。SPN是少见的交界性恶性潜能小儿胰腺肿瘤，治疗方法为手术切除肿瘤，对于儿童体尾部的SPN保留脾脏的胰体尾切除是首选，可取得满意的效果。

The clinical data and follow-up information of 4 pediatric patients with pancreatic solid pseudopapillary neoplasm （SPN） admitted in the First Affiliated Hospital of Harbin Medical University between January 2000 and January 2016 were retrospective reviewed. Four patients were all girls aged 8 - 13 years. All cases were treated with surgical resection and the diagnosis was confirmed histopathologically. Patients were followed up for up to 6 years, and there was no recurrence detected. Pancreatic SPN in children is a potentially malignant borderline tumor. Complete surgical resection is the only option for this disease, and spleen preserving pancreatectomy is the first choice of operation with satisfactory results.