肝胆胰系统炎性肌纤维母细胞瘤三例报告

Inflammatory myofibroblastic tumor of the hepatobiliary pancreatic system： report of three eases and literature review

目的 通过病例回顾,提高对肝胆胰系统炎性肌纤维母细胞瘤的认识、诊断和治疗.方法 总结3例经病理证实的肝胆胰系统炎性肌纤维母细胞瘤患者的临床资料,并复习相关文献资料.结果 讨论的3例炎性肌纤维母细胞瘤患者,其中肝脏1例、胆囊1例、胰腺1例,临床表现无特异性,术前诊断难度大,均疑诊为恶性肿瘤,均行手术治疗,术后预后良好,无一复发.结论 炎性肌纤维母细胞瘤属良性肿瘤,在肝胆胰系统中罕见,临床表现不典型,影像学检查无特异性,确诊仍依赖于病理.手术为其有效的治疗手段.有复发倾向,术后随访有重要意义.

Objective To improve the understanding, diagnosis and treatment of inflammatory myofibroblastic tumor （IMT） of the hepatobiliary pancreatic system through the cases review. Methods The clinical data of three cases of pathologically-proved IMT of the hepatobiliary pancreatic system was reported and relevant literatures were reviewed. Results Among three cases of IMT discussed, there consisted of a case of liver, a case of gallbladder and a case of pancreas. The clinical manifestations were nonspecific, and the preoperative diagnosis was difficult. All the patients with suspected malignant tumors underwent surgical treatment. The prognosis was good, with no recurrence. Condusion IMT is a benign tumor and is rare in hepatobiliary pancreatic system. The clinical manifestations are not typical and the imaging examinations are not specific. Its diagnosis depends on pathology. Surgery is an effective treatment. IMT has a tendency of recurrence, and its postoperative follow-up is of great significance.