韧带样型纤维瘤病的影像学表现

Imaging manifestations of desmoid-type fibromatoses

目的探讨韧带样型纤维瘤病(DF)的影像学表现。方法回顾分析经手术病理证实的17例DF的影像学表现,分析其CT或/和MRI特征。结果 17例均为单发病变,其中腹壁外型10例,腹壁型5例,腹内型(肠系膜)2例,共进行了10次CT、10次MRI检查,其中3例均行CT和MRI检查。CT检查10例,9例平扫呈等密度,密度均匀,1例腹内型DF平扫局部呈稍高密度;增强扫描5例,其中4例为轻度强化,另1例腹内型DF增强呈环形明显强化;2例延迟扫描呈渐进性强化。MRI检查有10例,T_1WI均为等信号,9例T_2WI、SPIR序列为高信号,内部信号欠均;1例腹内型DF内部见斑片状短T2低信号,SPIR呈低信号。6例DF行增强扫描,病灶呈中度、明显不均匀强化,内部可见点状、条索状、片状无强化区。结论 DF的CT、MRI表现具有一定的特征性,MRI更能反映病灶内组织学特点。

ObjectiveTo investigate imaging manifestations of desmoids type fibromatoses （DF）. MethodsThe CT and MRI features of 17 cases with DF were reviewed retrospectively. ResultsAll of 17 cases were solitary lesions, of which 10 cases were abdominal wall shape, 5 cases were abdominal wall type and 2 cases were intra abdominal （mesentery） type. In all the cases, 10 times CT and 10 MRI examinations were performed, of which 3 cases underwent CT and MRI examination. In 10 cases with CTexamination, 9 cases of plain scan was density, uniform density, 1 cases of abdominal DF scan showed slightly higher local density. Enhanced CT scanning was performed in 5 cases, including 4 cases of mild enhancement, and the other 1 case of intra abdominal DF showed annular enhancement. 2 cases of delayed scan showed progressive enhancement. MRI examination was performed in 10 cases, T1WI were equal signals, 9 cases of T2WI and SPIR sequences were high signals, and internal signals were not uniform. One case of internal DF showed patchy, short T2 low signal, and SPIR was low signal. 6 cases of DF underwent enhanced scan, the lesions showed moderate and markedly inhomogeneous enhancement, with punctate, funicular and patchy enhancement in the interior zone. ConclusionThe CT and MRI features of DF have some characteristics, and MRI can reflect the histological features of lesions.