腹壁型韧带样纤维瘤病的MSCT表现

MSCT manifestations of abdominal wall type desmoids-type fibromatoses

目的探讨腹壁型韧带样纤维瘤病(abdominal wall type desmoids-type fibromatoses,DF)的MSCT表现,并评价MSCT在诊断DF及鉴别诊断的价值。方法回顾性分析经病理证实的DF患者12例MSCT表现,包括肿瘤部位、大小、形态、边缘、CT密度及强化特征。结果 12例均位于腹前壁肌肉,横截面积最大约14.6cm×14.3cm,最小3.5cm×1.8cm,椭圆形8例,浅分叶状4例,边界清楚2例,模糊10例。MSCT平扫示12例全部呈稍低密度,密度较均匀,肿块均未见明显出血、囊变、坏死及钙化,有10例平扫可见少量条状稍高密度影。肿块增强后呈渐进性轻、中度强化,其中有6例增强后可见斑片状更高强化区,条状影未见明显强化。结论腹壁型韧带样纤维瘤MSCT表现具有特征性,正确的认识能为DF的诊断及鉴别提供重要价值。

Objective To investigate the MSCT manifestations of abdominal wall type desmoids-type fibromatoses, and to e- valuate the value of MSCT in the diagnosis of DF and differential diagnoses. Methods A retrospective review of 12 cases of DF proved by histopathology was performed. Images were reviewed with respect to location, size, shape, edge, CT density and rein- forcement characteristics. Results 12 cases were all located in the anterior abdominal wall muscles. The maximum size was 14.6 cmx 14.3 cm, the minimus size was 3.5 cm x 1.8 cm, 8 cases were elliptic, 4 cases were shallow lobulated, clear border was found in 2 cases, fuzzy in 10 cases. MSCT scan in all 12 cases were in slightly low density and the density was homogeneous, there were no obvious hemorrhage, cystic, necrosis and calcification, 10 cases can be found a small amount of strip-shaped slight- ly high density shadow. Enhanced scan was progressive mild or moderate enhancement, higher visible patchy enhancement area can be seen in 6 cases, the strip shadow was not seen obvious reinforcement. Conclusion CT manifestations of abdominal wall type desmoids-type fibromatoses have some characteristic, which is important to understanding correctly for the diagnosis and dif- ferential diagnosis of DF.