横纹肌样脑膜瘤MRI表现并文献复习

Analysis and comparison between MRI findings of rhabdoid meningioma and literature review

目的 :探讨横纹肌样脑膜瘤的MRI表现与病理特点的相关性,结合文献报道提高对本病的影像诊断水平,减少漏诊及误诊。方法:回顾性分析本院经手术病理证实的2例横纹肌样脑膜瘤患者的临床及MRI影像资料,并结合相关文献报道9例。结果:本组病例女7例,男4例,均为单发,7例囊实性,4例实性,实性部分T1WI主要呈等信号,T2WI主要呈稍高信号,囊性部分T1WI主要呈低信号,T2WI主要呈高信号,增强扫描2例均匀强化,9例不均匀强化,内有坏死囊变区,6例有"脑膜尾征",5例瘤周可见迂曲血管且肿瘤内可见流空信号,6例瘤周见明显水肿区。病理显示肿瘤绝大部分由横纹肌母细胞样瘤细胞构成。瘤组织内常出现坏死、出血、血管增生。结论:横纹肌样脑膜瘤MRI表现为实性或囊实性,特征是肿瘤内或瘤周可见低信号流空影及瘤周可见不同程度的水肿,但因其缺乏特异性,最终确诊还需依赖病理学检查。

Objective： To study the MRI findings of rhab doid meningioma in order to improve the diagnostic rate and re-duce misdiagnosis. Methods： A retrospective analysis of 2 rhabdoid meningiomas confirmed by surgery and pathology, com-bined with 9 cases reported in the literature, were studied. Results： Among the 11 cases of rhabdoid meningioma, 7 of them were female, 4 of them were male. Eleven tumors were solitary, 7 of them were cystic, and 4 of them were mixed. The solid part of tumor mainly showed equal signal in T1WI, while in T2WI it showed slightly hyperintensity. The cystic part of tumor showed hypointensity in T1WI and hyperintensity in T2WI. Two rhabdoid meningiomas showed uniform enhancement, 9 cases showed inhomogeneous enhancement. Six tumors presented with dural tail sign. Five of them showed peritumoral vascular tor-tuosity and flow void signal. While 6 of them showed peritumoral edema. Pathology revealed by most of rhabdomyoblasts like tumor cells constitute. The tumor tissues were easily found by necrosis, hemorrhage and vascular. Conclusion： The rhabdoid meningioma showed solid or cystic appearance on MRI, is characterized in or around the tumor showed low signal void shad-ow and peritumoral edema in different degree, but because of the lack of specific feature, the final diagnosis depends on pathological examination.