隆突性皮肤纤维肉瘤21例临床分析

Clinical Analysis of 21 Patients of Dermatofibrosacoma Protuberans

目的分析隆突性皮肤纤维肉瘤的临床特征,探讨其治疗方法。方法回顾性分析该21例患者的临床表现,误诊情况,病理表现,影像学(包括胸片、彩超、MRI)及治疗和转归等资料,进行描述性分析。结果 21例隆突性皮肤纤维肉瘤患者中男9例,女12例;初诊误诊13例(61.90%),21例均以扩大3cm进行手术切除,术后放疗,随访1~5年,复发2例;结论隆突性皮肤纤维肉瘤以单一红色结节为原发皮损,容易误诊,不易发生转移,行扩大切除术+辅助放疗是治疗隆突性皮肤纤维肉瘤的主要治疗方法。

Objective To analyze the clinical features and treatment of dermatofibrosarcoma protuberans. Methods The clinical manifestations, misdiagnosis, pathological features, imaging（including chest radiography, color Doppler ultrasound, MRI）, treatment and prognosis of the 21 cases were analyzed retrospectively.Results There were 21 cases of patients with dermatofibrosarcoma protuberans, including 9 males and 12 females.13 cases were misdiagnosed at first visit（61.90%）.Surgical resection of the enlarged 3cm was performed in 21 cases,and postoperative radiotherapy was made, and the follow-up last for 1 to 5 years; 2 cases were relapsed.Conclusion Primary lesion of Dermatofibrosarcoma protuberans is a single red nodules, so it is easy to misdiagnose.However, it is not easy to transfer.Enlarge excision plus auxiliary radiotherapy in treatment are the main treatment of fibrosarcoma.