乙状结肠肠壁囊样积气症合并肠梗阻1例

Pneumatosis cystoides intestinalis of the sigmoid colon complicated with intestinal obstruction:a case report

回顾性分析南京医科大学附属明基医院1例通过手术切除病理确诊的乙状结肠肠壁囊样积气症(pneumatosis c ystoides intestinalis,PCI)合并肠梗阻患者的临床资料及其病理学特征,结合国内外文献复习,总结其病因、病理学特征、临床表现、诊断及治疗进展。PCI是一种罕见的消化系统疾病,指发生在肠壁黏膜下和/或浆膜下及肌层的多发性充气囊肿,常无症状或表现缺乏特异性,临床易造成漏诊及误诊。近年来检查技术的提升及临床对PCI的进一步认识能有效提高诊断的准确率。

The report retrospectively analyzed the clinical data and pathological characteristics of one case of pneumatosis cystoides intestinalis of the sigmoid colon complicated with intestinal obstruction confirmed by pathological diagnosis, reviewed other cases from the related literature, and summarized the pathogenesis, pathological characteristics, clinical manifestations, diagnosis, and treatment progress. Pneumatosis cystoides intestinalis （PCI） is a rare disease of digestive system characterized by the presence of multiple gas-filled cysts in the intestinal submucosa and/or subserosa and/or muscularis. PCI was often missed diagnosis or misdiagnosed in clinic because it is usually asymptomatic or with no specific clinical manifestation. Strengthening the most understanding of PCI in clinic can effectively improve the accuracy of diagnosis with the improvement of inspection methods in recent years.