摘要
卡梅现象也称卡梅综合征，是发生于卡波西样血管内皮瘤或丛状血管瘤，并以严重血小板减少和消耗性凝血功能障碍为特征的临床综合征。该病较为罕见，多发于婴幼儿，病情凶险，得不到及时治疗者，可危及生命。该文对卡梅现象的临床表现、发病机制、诊断及治疗等方面的研究进展进行综述。
Kasabach - Merritt phenomenon（KMP）, also known as Kasabach - Men＇it＊ syndrome,is a rare syndrome associated with Kaposiform haemangioendothelioma or tufted angioma, and characterized by thrombocytopenia and consumptive coagulopathy. KMP onsets early and progresses quickly. If diagnosis and treatment delayed,it can be life-threatening. In this paper, the progress of clinical manifestations, pathogenesis, diagnosis and treatment of KMP are summarized.
作者
赵亚梅
高怡瑾
Zhao Yamei, Gao Yijin.(Department of Blood Oncology, Shanghai Children＇s Medical Center,Medical School of Shanghai Jiaotong University, Shanghai 200127, Chin)
出处
《国际儿科学杂志》
2018年第3期224-227,共4页
International Journal of Pediatrics
关键词
卡梅现象
卡波西样血管内皮瘤
丛状血管瘤
儿童
Kasabach-Merritt phenomenon
Kaposiform hemangioendothelioma
Tufted angioma
Child
