肾血管平滑肌脂肪瘤的治疗进展

Progress in Treatment of Renal Angiomyolipoma

肾血管平滑肌脂肪瘤（renal angiomyolipoma,RAML）作为一种常见的肾良性肿瘤,有多种治疗方式,包括保守治疗、药物治疗、微创介入治疗（消融术、肾动脉栓塞术）以及手术治疗（肾切除术和保留肾单位手术）,均有良好疗效。近年来新的技术理念层出不穷,大于4cm肿瘤不主张早期干预,雷帕霉素靶蛋白（m TOR）抑制剂治疗结节硬化症（tuberous sclerosis,TS）取得显著效果,手术治疗新技术不断发展,微创介入治疗适应证更加宽泛,本文就以上进展进行综述以期指导临床。

Renal angiomyolipoma（RAML） is a common benign neoplasm,which can be managed with conservative treatment,drug therapy,minimally invasive interventional therapy（ablation,renal artery embolization）,and surgical treatments（nephrectomies and nephron-sparing surgery）.This article reviews the recent progresses of new therapeutic ideas and modalities for RAML ：there is no need of early intervention for tumors larger than 4 cm;the m TOR inhibitors are effective for tuberous sclerosis（TS）;the newly developed surgical techniques are available;and the indications for minimally invasive interventions are broadened and so on.