Kartagener综合征的CT诊断及鉴别诊断

CT features and differential diagnosis of Kartagener syndrome

目的探讨Kartagener综合征(KS)的CT表现及鉴别诊断。方法回顾性分析14例KS患者胸部及副鼻窦CT图像,分析内容包括内脏反位、支气管扩张形态及伴随病变、副鼻窦炎症累及部位等。结果 14例KS均行胸部HRCT扫描,表现为全内脏反位及不同程度的支气管扩张,9例呈囊柱状改变,3例出现"印戒征",2例出现"蜂窝征",伴随病变包括:弥漫性细支气管炎,肺部感染,胸腔积液,肺气肿等。7例完全型KS患者中,3例为全组副鼻窦炎症,4例为两侧上颌窦炎症伴筛窦、额窦或蝶窦炎症。7例不完全型KS患者不伴副鼻窦炎。结论 Kartagener综合征具有典型的支气管扩张、内脏反位及副鼻窦炎的表现,CT是诊断KS最有价值的方法之一。

Objective To explore the imaging findings of kartagener syndrome.Methods The CT findings of 14 KS patients were retrospectively analyzed. Results 14 KS patients with classical triad （bronchiectasis, sinuses and situs inversus） went through CT scan. HRCT findings of bronchiectasis can be tubular/cylindrical or saccular/cystic. Accompanying lesions included diffuse bronchitis, pulmonary infection, pleural effusion, emphysema, etc. In 7 patients of typical KS, 3 patients were complicated with pansinusitis, while the other 4 patients demonstrated maxillary sinusitis with ethmoid, frontal or sphenoid sinusitis. Sinusitis were absent in another 7 atypical KS patients.Conclusion Kartagener syndrome is characterized by the clinical triad of bronchiectasis, situs inversus, pansinusitis. CT scan is tended to have great value in demonstration of those lesions.