摘要
Background:Aggressive angiomyxoma (AAM) is a rare semimalignant tumor o f the s oft tissue predominantly occurring in the genital and pelvic area. It tends to o ccur more frequently in premenopausal women and it is characterized by slow grow th and local infiltrative aggressiveness. It has a considerable risk for local r ecurrences. Patient and Method: We report the case of a 30-year-old female who had a pelvic tumor for a period of 4 years without adequate therapy before atte nding our hospital. During this period, the tumor was misdiagnosed first as a Ga rdner-cyst, later as fibromatosis. Several surgical attempts did not result in complete resection. In July 2002we performed a laparotomy and complete tumor red uction, preserving fertility potential. Histological examination revealed an agg ressive angiomyxoma. The patient remained well after operation and no menstrual or coital problems occurred. Conclusion: An extended case history of progressive tumor growth should not take 4 years to diagnose. Anational registry should be established to aid the diagnosis of rare gynecological tumors. The treatment of such tumors should take place in specialized centers.
Background:Aggressive angiomyxoma (AAM) is a rare semimalignant tumor o f the s oft tissue predominantly occurring in the genital and pelvic area. It tends to o ccur more frequently in premenopausal women and it is characterized by slow grow th and local infiltrative aggressiveness. It has a considerable risk for local r ecurrences. Patient and Method: We report the case of a 30-year-old female who had a pelvic tumor for a period of 4 years without adequate therapy before atte nding our hospital. During this period, the tumor was misdiagnosed first as a Ga rdner-cyst, later as fibromatosis. Several surgical attempts did not result in complete resection. In July 2002we performed a laparotomy and complete tumor red uction, preserving fertility potential. Histological examination revealed an agg ressive angiomyxoma. The patient remained well after operation and no menstrual or coital problems occurred. Conclusion: An extended case history of progressive tumor growth should not take 4 years to diagnose. Anational registry should be established to aid the diagnosis of rare gynecological tumors. The treatment of such tumors should take place in specialized centers.
