摘要
多囊性肾细胞癌在成人是一种非常罕见的疾病,在儿童年龄群体中先前未见报道。作者报道了1例患右侧肾囊肿的8岁女孩,由于患侧肾脏广泛受累而接受了肾切除手术。术后的组织病理学检验结果证实所有的囊肿中都存在肾癌细胞。在儿科警惕恶性肿瘤的存在是极其重要的,因为在最近的报道中提倡对单侧的肾囊肿进行保守性等待和观察处理,而单侧肾囊肿与肾细胞癌有着相似的临床和影像学表现。
Multilocular cystic renal cell carcinoma is an extremely rare condition in adults with no previous case reports in the pediatric age group. The authors report on an 8 - year-old girl who underwent nephrectomy for a right-sided renal cystic disease because of extensive involvement of the kidney. Subsequent histopathologic examination findings showed presence of renal cell carcinoma in all the cysts. Awareness of this malignancy in a child is extremely important in the background of recent reports advocating conservative wait and watch management in unilateral renal cystic disease, which has similar clinical and imaging findings.
