摘要
Superior canal dehiscence syndrome is a newly recognized syndrome characterize d by vertigo and nystagmus induced by sound (Tullio phenomenon) or changes of mi ddle ear (Hennebert sign) or intracranial pressure. We report on a patient with bilateral superior canal dehiscence syndrome who presented with unusual manifest ations including pulse synchronous vertical pendular nystagmus and Valsalva in duced, up and counterclockwise beating jerk nystagmus. These unusual symptoms m ay be a clue to a better understanding of the pathophysiology of superior canal dehiscence syndrome. Abnormal communication between the inner ears and the intra cranial space may explain the vertical pendular and pulse synchronous nystagmus , modulated by increased intracranial pressure.
Superior canal dehiscence syndrome is a newly recognized syndrome characterize d by vertigo and nystagmus induced by sound (Tullio phenomenon) or changes of mi ddle ear (Hennebert sign) or intracranial pressure. We report on a patient with bilateral superior canal dehiscence syndrome who presented with unusual manifest ations including pulse synchronous vertical pendular nystagmus and Valsalva in duced, up and counterclockwise beating jerk nystagmus. These unusual symptoms m ay be a clue to a better understanding of the pathophysiology of superior canal dehiscence syndrome. Abnormal communication between the inner ears and the intra cranial space may explain the vertical pendular and pulse synchronous nystagmus , modulated by increased intracranial pressure.
