阿-希二氏畸形合并脊髓空洞症的MRI研究

The Studies of Chiari Malformation with Syringomyelia in MRI

目的:利用MRI技术,研究Chiari Ⅰ畸形合并脊髓空洞症的影像学特征。材料与方法:回顾性分析经MRI证实的Chiari Ⅰ畸形55例,其中7例经手术治疗。用Siemens 1.0T MR扫描仪,对脊髓和后颅凹进行矢状和横断面扫描,选择SE T_1WI和T_2WI成像序列。结果:55例Chiari Ⅰ畸形患者中,小脑扁桃体下疝长度为6～25mm,平均9mm。合并脊髓空洞症42例(76％),其中30例(71％)有脊髓增粗,这多发生在无间隔的空洞中。呈“串珠样”改变者,脊髓径正常或变细。小脑扁桃体下疝的长度与脊髓增粗和脑室扩大无相关性。经手术治疗的7例中,5例扁桃体下疝消失,2例症状改善。1例复发。结论:MRI技术可以对Chiari Ⅰ畸形和脊髓空洞症患者提供术前影像学诊断,并可进行术后追踪观察。

Purposes: To study the MRI Characteristics in Chiari malformation with Syringomyeli-a. Materials and Methods: The saggital and transverse MRI (SE T1WI, T2WI) of the spina and the postorior cranial forssa were scaned (Siemens 1.0T MRI) in 55 cases of Chiari malformation with syringomyelia. The MRI findings were analysed retrospectively. Results: The length of the herniated tonsils was 6 - 25mm with a mean of 9mm. In all the cases, syringomyelia were presented in 42 cases (76% ), of 30 cases (71% ) with noninterval syringomyelia presented with expansion of the spinal cord. Of 55 cases the spinal cords with string beads were normal or slightly slim in size. The length of the herniated tonsils was unrelated with degree of the expansion of the spinal cord and ventrical. In 5 of the 7 patients undergone surgical treatment, the herniated tonsils disappeared. The Syringomyelia were improved in 2 of the 7 cases. On follow - up study recurred herniated tonsils was found in one case. Conclusions: This study revealed that MRI was playing an important role in pre - and -post operation of patients with chiari malformation.