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马凡综合征并主动脉夹层DeBakeyⅠ型死亡病例1例 被引量:2

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摘要 1病例患者,男性,31岁,主因“突发胸背部疼痛1h”于2016-03-18,23时入院。患者1h前打篮球时突发剧烈胸痛,持续性,位于心前区,伴后背部放射,伴大汗、心慌、胸闷、呼吸困难,无黑曚、晕厥、恶心、呕吐等不适。既往:否认高血压、冠心病、糖尿病等病史,母亲患马凡综合征猝死。查体:T:36.5℃,BP:114/40mmHg(1mmHg=0.133kPa),HR:61次/min,R:19次/分,SPO2:91%。神清,表情痛苦,身高190cm,四肢细长,拇指征、指腕征(+),双肺呼吸音清,未闻及明显干湿罗音,心律齐,心率61次/min,心音稍低,主动脉瓣听诊区可闻及舒张期杂音,腹部未见阳性体征,左侧足背动脉搏动稍差,双下肢无水肿。急诊CT示:主动脉夹层(DebakeyⅠ型)。初步诊断为:①马凡综合征;②主动脉夹层DebakeyⅠ型。
作者 李方 熊世熙
出处 《中国循证心血管医学杂志》 2017年第1期108-109,共2页 Chinese Journal of Evidence-Based Cardiovascular Medicine
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