肺淋巴管肌瘤病并发气胸1例并文献回顾

A Case of Pulmonary Lymphangiomyomatosis Complicated With Pneumothorax and Literature Review

目的肺淋巴管肌瘤病为重症监护病房极其罕见的一种疾病,通过个案报道及文献复习,使大家对该疾病的认识更加深入。方法对我科收治的1例肺淋巴管肌瘤病的一些治疗体会结合文献相关知识对该疾病进行治疗经验总结。结果肺淋巴管肌瘤病在重症监护病房极其罕见,死亡率极高,需加强该病的认识,及时判断患者预后。结论肺淋巴管肌瘤病病情危重,入住重症监护室后应该积极加强抗感染,加强器官功能维护,肺移植是一条可供选择的治疗方法。

Objective Pulmonary lymphangiomyomatosis is an extremely rare disease in intensive care unit,and it is more important to understand the disease through case report and literature review.Methods Some therapeutic experiences in the treatment of lymphangiomyomatosis of the lung in my department were summarized in this paper.Results Pulmonary lymphangiomyomatosis is extremely rare in intensive care unit,and the mortality rate was extremely high,so it was necessary to strengthen the understanding of the disease and timely judge the prognosis of patients.Conclusion Pulmonary lymphangiomyomatosis is critically ill,and should be actively strengthened to strengthen the function of organ maintenance after admission to intensive care unit,and lung transplantation is an alternative treatment.