肝血管平滑肌脂肪瘤1例报告及文献复习

Hepatic angiomyolipoma:A case report and literature review

目的:探讨1例肝脏血管平滑肌脂肪瘤(HAML)患者的临床特点和诊断,分析总结其诊断及治疗方法。方法:回顾性分析1例HAML误诊为肝癌患者的临床资料,并进行相关文献复习。结果:1例中年女性患者因腰背部不适就诊于本院,行上腹部CT和MRI检查发现肝左叶内下段占位性病变,考虑原发性肝细胞癌,给予手术切除治疗,患者术后病理组织学检查以及免疫组织化学染色诊断为上皮样型HAML,患者术后恢复良好,随访至今未见肿物再发。结论:HAML无特异性的临床特点及影像学表现,其诊断主要依靠组织病理学检查,手术切除是有效的治疗方法。

Objective:To discuss the clinic features and diagnosis of one case of hepatic angiomyolipoma(HAML),and to analyze and summarize its diagnosis and treatment methods.Methods:The clinical materials of one case of HAML patient who was misdiagnosised as hepatocellcular carcinoma were analyzed retrospectively,and the related literatures were reviewed.Results:A middle-aged female patient visited our outpatient service because of low back discomfort.The upper abdominal CT and MRI suggested that a space occupying lesion located at the left lobe of liver inner lower segment,considering a high possibility of hepatocellular carcinoma.The patient underwent the left lobe of inner lower segmentectomy.The postoperative histopathological examination and immunohistochemical staining showed the tumour was HAML,After operation,the patient recovered well and the follow-up examination after hepatectomy found no tumor recurrence.Conclusion:HAML has no specific clinical characteristics or imaging features.The diagnosis of HAML mostly depend on the histopathological examination and hepatectomy is the effective treatment.