儿童肾脏囊性疾病的诊治进展

Progress of diagnosis and treatment for cystic kidney disease in children

肾脏囊性疾病是儿童肾脏发生囊性改变的主要疾病。此类疾病可能是由非遗传性胎儿畸形或遗传性疾病导致的,极少数可能为获得性的。囊肿可能呈孤立性表现,或是某综合征的表现之一。大多数肾囊肿通常是孤立而不危及生命的;然而,致命的肾脏囊性疾病也可从这些占位性病变发展而来。虽然肾脏囊性疾病的表现相似,但其有不同的特点,预后各异。如何早期正确地诊断这类疾病,要准确地掌握其发病机制、病理基础、临床特点及影像学表现。现就儿童常见的肾脏囊性疾病进行全面的分析,以帮助临床医师对此类疾病进行早期识别及有效管理。

Cystic kidney disease is the main disease of cystic kidney change in children.It may be caused by non-genetic fetal malformations or genetic diseases, or may be acquired rarely.Most renal cysts are usually isolated oraspart of a syndrome.However, fatal renal cystic diseases can develop from these space occupying lesions.Although renalcystic diseases are similar in presentation, they possess distinct features and variable prognosis later in life.In order to correctly diagnose this kind of disease in the early stage, it claim to accurately grasp its pathogenesis, pathology, clinical characteristics and radiological findings.A comprehensive analysis of common cystic kidney disease in children is carried out to help clinicians to aid in early distinction and appropriate treatment.