子宫血管周上皮样细胞肿瘤一例报告及文献复习

A Case Report of Perivascular Epithelioid Cell Tumor of Uterus and Literature Review

血管周上皮样细胞肿瘤(PEComa)是一种临床少见的间叶性肿瘤,生物学特性多样,恶性潜能未确定,发生于子宫极为罕见,术前极易漏诊、误诊,临床医生必须给予足够重视。为提高对此病的认识,现对1例子宫PEComa患者资料进行回顾分析,并复习相关文献,进一步探讨其临床表现、病理特点、免疫表型、治疗及预后,以加深临床医生对此病的认识,并提高诊治能力。

Perivascular epithelioid cell tumor (PEComa) is a rare clinical mesenchymal tumor with diverse biological characteristics and undetermined malignant potential. It is extremely rare in the uterus and is easily misdiagnosed before surgery. Clinicians must pay enough attention. Therefore, we now review the data of a patient with uterine PEComa, and review the relevant literature to further explore its clinical manifestations, pathological features, immunophenotype, treatment and prognosis,in order to deepen the understanding of this disease and improve the ability to diagnose and treat.