摘要
多发性内分泌腺瘤病1型(multiple endocrine neoplasia type1, MEN1)是一种累及2个及以上内分泌腺体的肿瘤综合征,甲状旁腺、胰腺及垂体为最常累及的腺体,其中胰血管活性肠肽瘤(vasoactive intestinal peptide tumor, VIPoma )极其罕见,VIPoma最早于1958年由Verner和Morrison报道[1],发病率约为1/1000万[2],约占MEN1的5%[3],以顽固性水样腹泻、低钾血症、无胃酸或低胃酸分泌的综合征(WDHA综合征)为特点。
作者
郭小青
高月
薛建锋
王晓娟
任高飞
刘艳霞
邢晶晶
栗夏莲
Guo Xiaoqing;Gao Yue;Xue Jianfeng;Wang Xiaojuan;Ren Gaofei;Liu Yanxia;Xing Jingjing;Li Xialian(Department of Endocrinology,the First Affiliated Hospital of Zhengzhou University,Zhengzhou 450000,China;Department of Hepatobiliary Pancreas,the First Affiliated Hospital of Zhengzhou University,Zhengzhou 450000,China;Department of Pathology,the First Affiliated Hospital of Zhengzhou University,Zhengzhou 450000,China)
出处
《中华内分泌代谢杂志》
CAS
CSCD
北大核心
2019年第4期337-340,共4页
Chinese Journal of Endocrinology and Metabolism