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脂肪营养不良综合征3例报道及文献复习

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摘要 1病例资料患者,男,42岁,2015年10月就诊于某三甲医院,主诉“发现左下肢前侧凹陷20余天”,肌电图、神经电图及有关结缔组织病血液检查均未见异常,按神经源性肌萎缩治疗无效。来我院查体:左下肢股前侧一约7cm×10cm大小凹陷,凹陷区可触及肌肉轮廓和骨骼,皮肤、毛发正常(图A)。左下肢MRI示:左下肢股前部脂肪信号消失,双侧肌肉体积对称,扫描范围内骨骼、肌肉未见异常信号(图B、图C)。病理活检示:表皮真皮层大致正常,皮下脂肪层缺失,纤维肌肉组织未见异常。
作者 李静 屈宝华
出处 《皮肤病与性病》 2019年第4期578-580,共3页 Dermatology and Venereology
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