性腺外原发卵黄囊瘤的临床及影像特征

Primary Yolk Sac Tumor of Extra-Gonadal Organ:CT/MRI and Clinical Features

目的分析性腺外原发卵黄囊瘤(YST)的临床及影像学表现特征,以提高对该病的认识及诊断水平。方法回顾性分析经病理证实的26例性腺外原发YST患者的临床与影像资料,总结其临床、CT及MRI特点。结果性腺外单纯型YST 24例,混合型2例;肿瘤位于胸腹部23例(其中纵隔14例,骶尾部5例,腹膜后3例,前腹部1例),颅内3例(左侧侧脑室、鞍区、松果体各1例);CT/MRI表现为椭圆形或不规则形肿块,囊实性或实性,实性成分不均匀中度-明显强化,囊性成分无强化,6例见迂曲供血动脉。结论性腺外YST影像表现具有一定特征,结合临床相关资料能提高诊断的准确性。

Objective To analyze the clinical and imaging features of extra-glandular primary yolk sac tumor(YST) in order to improve the understanding and diagnosis of the disease. Methods The clinical and imaging data of 26 patients with extra-gonadal YST confirmed by pathology were retrospectively analyzed. The clinical, CT and MRI features were summarized. Results The pathology of primary YST consisted of 2 types including 24 cases with single component and 2 cases with mixed components,The tumors were located in the mediastinum(n=14),sacrococcygeal region(n= 5),retroperitoneum(n=3),anterior abdomen(n=1),left parococele(n=1),saddle area(n=1),pineal body(n= 1). PrimaryYST mostly presents as solid or solid-cystic mass that is ill defined,with mild or significant enhancement. Feeding blood vessels were observed in 6 cases. Conclusion Primary YST has characteristic CT/MRI images,which are helpful for the diagnosis of YST combining with clinical fetures.