摘要原发性中枢神经系统血管炎(primary central nervous system vasculitis,PACNS),又被称为脑血管炎,是指发生于脑部的病因未名、非感染性、非自身免疫性、不伴有其他系统性疾病,累及脑部的中小血管和软脑膜血管壁,临床症状主要表现为中枢神经系统损害症状[1]。临床症状主要表现为中枢神经系统损害症状。
3Castle J, Linas R, Wityk R, et al. Biopsy proven isolated CNS vasculitis, much vaunted but rarely seen: 20 years retrospective review of brain biopsis[J]. Stroke, 2008,39 : 574-582.
4de Boysson H, Zuber M, Naggara O, et al. promary angiitis of the central nervous system:decription of the firsy fifty-two a dults enrolled in the French cohort of patients with promary vasculitis of the central nervous system[J]. Arthritis pheuma tol,2014,66(5):1 315-1 326.
5Powers WJ. Primary angiitis ot" the central nervous system: di agnostic criteria[J]. Neurol C1in,2015 ,38(2):515-526.
6Bajaj BK,Pandey S, Ramanujam B, et al. Primary angiitis of central nervous system: The story of a great masquerader[J]. J Neurosci Rural pract,201S,6(3):399-401.
7Salvarani C, Brown RD Jr, Christianson TJ. Mycophenolate mofetil in primary central nervous system vasculitisrJ:. Semin Arthritis Rheum, 2015,45(1) :55 -59.
8Neel A, Auffray Calvier E, Guillon B, et al. Chanllenging the diagnosis of primary angiitis of the central nervous system: a single-center retropective study[J]. J Rheumatol, 2012,39 ( 5 ) : 1 026-1 034.
9Salvarani C, Brown RD, Huston J, et al. Treanment of primary CNS vasculitis with rituximab: case report [J]. Neurology, 2014,82(14) :1 287-1 288.
10Hirano K, Fukae J, Hieda S, et al. Eosinophilic meningitis cause by promary angiitis of the central nervous system[J]. Intern Med,2013,52(12):1 393-1 396.
