双胎妊娠合并心肌致密化不全心肌病一例

Twin pregnancy with noncompaction of the ventricular myocardium:a case report

心血管疾病是非产科因素致孕产妇死亡的重要病因。心肌致密化不全(NVM)是一种罕见的先天性心肌病,心力衰竭、心律失常及血栓栓塞是其严重并发症,经胸超声心动图检查是其主要诊断方法。目前妊娠合并心肌致密化不全心肌病以对症用药为主要治疗方法,同时需考虑母儿安全性,综合病情以剖宫产终止妊娠为宜。本文对1例双胎妊娠合并心肌致密化不全心肌病患者的诊疗过程进行报告,并结合国内3例妊娠合并心肌致密化不全心肌病病例进行分析,旨在提高对妊娠期该疾病的临床认知和诊疗水平。

Cardiovascular disease is an important cause of maternal death with non-obstetric factors.Noncompaction of the ventricular myocardium(NVM)is a rare congenital cardiomyopathy.The serious complications are heart failure,arrhythmia,and thromboembolism.Transthoracic echocardiography is the main diagnostic method.At present,the maintreatment method of pregnancy combined with NVM is control symptom by medication.Meanwhile,the safety of mother andinfant should be considered.It is considered appropriate to terminate pregnancy by cesarean section.This article analyzedthe diagnosis and treatment of three cases of pregnancy with NVM and one case of twin pregnancy with NVM reported in ourhospital,hoping to improve the clinical cognition and diagnosis of this disease during pregnancy.