特发性肺间质纤维化诊治进展

Progress in diagnosis and treatment of idiopathic pulmonary fibrosis

特发性肺纤维化(IPF)是一种原因不明、进行性加重、最终发展为不可逆肺纤维化的常见的间质性肺疾病(ILD)。近年来,国际上发表了多篇有关IPF的诊治共识和指南。文章就IPF定义的变迁,诊断标准更新及治疗变化做一阐述。

Idiopathic pulmonary fibrosis(IPF)is a common interstitial lung disease(ILD)with unknown causes and progressive progression,and it could eventually development into irreversible pulmonary fibrosis.In recent years,a number of international consensus and guidelines on the diagnosis and treatment of IPF have been published.In this paper,the changes in the definition of IPF,as well as the update of its diagnostic criteria and treatment approaches are described.