儿童肺朗格汉斯细胞组织细胞增生症的CT表现

CT manifestations of pulmonary Langerhans cell histiocytosis in children

目的:探讨儿童肺朗格汉斯细胞组织细胞增生症(PLCH)的CT表现特点,以提高对该病的诊断准确率。方法:回顾性分析39例PLCH患儿的肺部CT表现。结果:39例中CT表现为肺部结节21例,囊腔14例,其中结节合并囊腔9例;表现为轻度肺间质病变17例。结节及囊腔均可单发或多发,单发或少量结节、囊腔以胸膜下分布为主,弥漫性结节、囊腔以肺上叶及肺外带、中带明显。结论:PLCH的CT表现以肺间质病变为主,结节、囊腔是其特征性表现,且分布具有一定特点;CT是诊断PLCH及判断治疗效果的重要方法。

Objective:To discuss the CT manifestations of pulmonary Langerhans cell histiocytosis(PLCH) in children,for well diagnosis in the disease.Methods:A retrospective study was performed on 39 patients with PLCH.Results:A total of 21 cases were pulmonary nodules,14 cases were pulmonary cysts,of which 9 cases were nodules and cysts.17 cases showed interstitial lung lesions.The pulmonary nodules and cysts were single or multiple,single or a small number of nodules,cysts were mainly distributed under the pleura,diffuse nodules,cysts were obvious in the upper lobe of the lung and the lung extraneous,middle zone.Conclusions:The CT manifestations of PLCH were mainly pulmonary interstitia l lesions,and nodules and cysts are characteristic manifestations with certain distribution characteristics.Therefore,CT is an important method to diagnose PLCH and judge the therapeutic effect.