促结缔组织增生性小圆细胞肿瘤伴多发转移的超声表现1例报告

Ultrasonic Manifestations of Desmoplastic Small Round Cell Tumor with Multiple Metastases:Case Report

促结缔组织增生性小圆细胞肿瘤(desmoplastic small round cell tumor, DSRCT)是一种好发于青少年的罕见恶性肿瘤,早期诊断困难,预后差。本文报道的1例DSRCT患者腹部包块超声表现为腹内病灶巨大,呈实性,边界欠清楚,形态不规则,内部无明显液化及钙化,血供不丰富。其包绕血管生长,但未见确切侵犯血管征象;肿瘤发生肝内及腹内淋巴结转移,肝内转移灶可见周边低回声晕;肿瘤包块压迫推挤邻近组织器官,引起双肾积水,对骨有破坏浸蚀征象。分析总结DSRCT的超声表现可提高临床对该疾病的认识,为诊断提供超声影像依据。

Desmoplastic small round cell tumor(DSRCT) is a rare malignant tumor, which is prone to occur in teenagersDesmoplastic small round cell tumor(DSRCT) is a rare malignant tumor that often occurs in adolescents. Early diagnosis is difficult and the prognosis is poor. In this case report, the ultrasonography of DSRCT showed that the huge solid mass was in the abdomen with unclear boundary, irregular shape, insufficient blood supply but without obvious liquefaction and calcification. The masses encircled the vessels, but no evidence of vascular invasion. Intrahepatic metastases with peripheral hypoechoic aureole and abdominal lymph node metastases were observed. The tumor mass compressed adjacent tissues and organs, causing bilateral hydronephrosis and bone erosion. In a word, the ultrasonographic characteristics could be used for diagnosing the DSRCT in the clinic.