子宫自然杀伤/T细胞淋巴瘤合并噬血细胞综合征一例并文献复习

Uterine Natural Killer/T-Cell Lymphoma Combined with Hemophagocytic Syndrome:A Case Report and Literature Review

子宫自然杀伤(NK)/T细胞淋巴瘤合并噬血细胞综合征临床极为罕见,其病情进展迅速、病死率高,是一种严重的高侵袭性疾病。该病的相关辅助检查结果及临床表现缺乏特异性,与生殖系统的其他恶性肿瘤难以鉴别,误诊率高。本文对恩施土家族苗族自治州中心医院于2020年3月收治的1例该病患者的病例资料进行回顾,并对该病的诊断及治疗方式进行讨论,以期减少该病的误诊、漏诊,改善患者预后。

The case of uterine natural killer/T-cell lymphoma combined with hemophagocytic syndrome is very rare in clinic.It is a serious and aggressive disease with rapid progress and high mortality.In addition,it is difficult to differentiate the disease from other malignant tumors of the reproductive system due to the non-specificity of the related auxiliary examination results and clinical manifestations,leading to a high misdiagnosis rate.To reduce misdiagnosis and missed diagnosis of the disease and improve the prognosis,the case data of a patient treated by the Central Hospital of Enshi Tujia and Miao Autonomous Prefecuture in March 2020 is introduced,and the methods of diagnosis and treatment are discussed.