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终末期肝病合并遗传性球形红细胞增多症并存地中海贫血1例 被引量:1

A case of end-stage liver disease with hereditary spherocytosis and thalassemia
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摘要 终末期肝病是指各种慢性肝病的晚期阶段,以黄疸、脾大、腹水、肝性脑病等临床表现为主。遗传性球形红细胞增多症和地中海贫血是归属于溶血性贫血。既往报道同时患有上述两种贫血的患者较少,且本例患者的黄疸、贫血与临床单一疾病的特征不符,为少见病例。 End-stage liver disease refers to the late stage of various chronic liver diseases,mainly clinical manifestations such as jaundice,splenomegaly,ascites,hepatic encephalopathy.Hereditary spherocytosis and thalassemia belong to hemolytic anemia.It has been reported that fewer patients suffer from the above two types of anemia.The jaundice and anemia of this patient do not match the characteristics of a single clinical disease,which is a rare case.
作者 张丽丽 胡建华 勾春燕 吕文良 ZHANG Li-li;HU Jian-hua;GOU Chun-yan;LU Wen-liang(Department of infectious diseases,Guang'anmen hospital,China academy of Chinese medical sciences,Beijing,100053,China;不详)
出处 《中西医结合肝病杂志》 CAS 2021年第1期23-25,共3页 Chinese Journal of Integrated Traditional and Western Medicine on Liver Diseases
基金 国家重点研发计划“中医药现代化研究”重点专项(No.2018YFC1705700) “扬帆计划”重点医学专业项目(No.ZYLX201819)。
关键词 终末期肝病 遗传性球形红细胞增多症 地中海贫血 end-stage liver disease hereditary spherocytosis thalassemia
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