子宫叶状分割性平滑肌瘤并静脉平滑肌瘤病一例

Cotyledonoid Hydropic Intravenous Leiomyomatosis:A Case Report

子宫叶状分割性平滑肌瘤并静脉平滑肌瘤病(CHIL)是一种罕见的良性子宫平滑肌瘤,为子宫叶状分割性平滑肌瘤(CDLU)累及血管,并具有静脉内平滑肌瘤(IVL)的特点。辅助检查主要表现为子宫壁出现低回声光团,血流丰富,剖腹探查可见血运丰富、灰红质软似胎盘小叶样的子宫肌瘤,肌瘤剔除过程中可见部分小血管受肌瘤侵蚀严重,可自小血管内牵出细长肌瘤样病灶。现报道1例CHIL,综合国内外文献,总结该病的诊断及治疗经验以指导临床。

The cotyledonoid hydropic intravenous leiomyomatosis(CHIL)is a rare benign uterine leiomyomatosis that involves the vessels of cotyledonoid dissecting leiomyoma of the uterus(CDLU).It may also be characterised by intravenous leiomyomatosis(IVL).The auxiliary examination mainly showed the appearance of low-echo light mass in the uterine wall and the rich blood flow.The exploratory laparotomy showed the uterine fibroids with rich blood circulation and soft grayish red like placental lobules.During the myoma elimination,some small vessels could be seriously damaged by myomas,and the slender myoma-like lesions could be brought out from the small vessels.We report a case of CHIL,review the literatures and summarize the diagnosis and treatment of this disease,so as to guide the clinical practice.