输尿管肌纤维发育不良的MRI表现与病理生理关系

Relationship between MRI findings and pathophysiology of ureteral myofibrous dysplasia

目的:探讨输尿管肌纤维发育不良的MRI的影像特征及病理生理间的联系。方法;回顾性分析阜阳市妇女儿童医院及第五人民医院1996年-2018年24例术前进行MRI+MRU检查的输尿管肌肉纤维发育不良的MRI表现,并与病理结果对照。结果:所有术前MR诊断与病理、手术所见符合,定位诊断符合率100%,定性诊断符合率95.8%。24例输尿管肌纤维发育不良,轻中度积水21例,重度积水3例。狭窄节段显示4例。狭窄节段未显示20例,其中狭窄端呈鸟嘴状或细线状12例,杵状5例,圆钝3例。结论:MRI平扫结合MRU价值对于输尿管肌纤维发育不良的诊断有价值,且无创、无辐射。

Objective:To investigate the relationship between magnetic resonance imaging(MRI)features and pathophysiology of ureteral myofibrous dysplasia.Methods:The MRI findings of 24 cases of ureteral myofibrous dysplasia in Fuyang Women's and Children's Hospital and the Fifth People's Hospital were retrospectively analyzed,and compared with the pathological results from 1996 to 2018.Results:All preoperative MRI diagnosis was consistent with pathology and operation,the coincidence rate of localization diagnosis was 100%,and the coincidence rate of qualitative diagnosis was 95.8%.In the 24 cases of ureteral myofibrous dysplasia,21 cases hadmild to moderate hydronephrosis,3 cases presented severe hydronephrosis.Stenotic segments were shown in 4 cases,while was not shown in 20 cases,including 12 cases with beak or thin-line-likestenosis,5 cases with pestle and 3 cases with round bluntstenosis.Conclusion:The value of MRI combined with magnetic resonance urography is valuable in the diagnosis of ureteral myofibrous dysplasia,and it is non-invasive and non-radiation.