外阴阴道壁血管肌纤维母细胞瘤二例及文献复习

Two Cases Report of Angiomyofibroblastoma in the Vaginal Wall and Vulva,with A Mini Review

血管肌纤维母细胞瘤(angiomyofibroblastoma,AMF)是一种罕见的良性软组织肿瘤,主要来源于盆腔软组织间叶细胞。好发于女性,临床表现无特异性,影像学检查使用率低且术前难以确诊,需依靠病理学明确诊断。一般以手术治疗为主,预后良好,复发率极低。现报告2例外阴阴道壁血管肌纤维母细胞瘤病例,探讨该病的临床特点、病理及免疫组化特征、诊治方法及预后情况,并回顾相关文献,加深对该病的认识。

Angiomyofibroblastoma(AMF)as a rare benign soft-tissue tumor is mainly caused by the interstitial cells of the pelvic soft tissue.It tends to occur in women,with non-specific clinical manifestations,low rate of imaging examination and difficulty in preoperative diagnosis.The clear diagnosis is dependent on pathology.Generally,surgery is the main treatment with a good prognosis and a very low recurrence rate.In this paper,two cases of angiomyofibroblastoma in the vaginal wall and vulva were reported.With a mini review,the clinical characteristics,pathological and immunohistochemical characteristics,diagnosis,treatment and prognosis of this disease were discussed.