婴儿眼眶黑色素性神经外胚瘤一例

Orbital melanotic neuroectodermal tumor in an infant

1例被家属发现左眼部肿物迅速生长1周的婴儿就诊眼科,查体发现左眼眶外上方形状不规则质硬肿物,B超显示病变为不均匀低回声区,边界欠清,眼眶CT显示左眼眶外壁颧骨眶突周围软组织肿物,局部骨质及泪腺受累;入院后于全身麻醉下行左眼眶肿物切除术,经组织病理学检查诊断为婴儿黑色素性神经外胚瘤。术后随访6个月,患儿身体良好,未见肿瘤复发。

A 3-month-old infant patient presented with a 1-week history of a quickly progressive mass in the left eye.A hard,irregularly shaped tumor was found in the superolateral orbit.B-scan showed an uneven hypoecho and an undefined lesion.On the orbital CT,a soft tissue mass was located around the left zygomatic tubercle,involving part of the bone and lacrimal gland.The left orbital mass was removed under general anesthesia after admission.The histological and immunohistochemical examination revealed it was a melanotic neuroectodermal tumor.The infant patient was followed up for 6 months after the operation,and no recurrence was found.