摘要
BACKGROUND Congenital biliary atresia is a type of obstruction of the bile ducts inside and outside the liver,which can lead to cholestatic liver cirrhosis and eventually liver failure.The preduodenal portal vein(PD-PV)is a rare developmental malformation of the PV.The PV courses in front of the duodenum.However,very few cases of neonatal biliary atresia combined with PD-PV have been reported in the scientific literature.CASE SUMMARY A 1-mo-and-4-d-old child was admitted to the hospital in January because of yellowish skin.After surgical consultation,surgical intervention was recommended.The child underwent Hilar-jejunal anastomosis,duodenal rhomboid anastomosis,and abdominal drainage under general anesthesia.During the operation,the PV was located at the anterior edge of the duodenum.CONCLUSION Diagnoses:(1)Congenital biliary atresia;(2)PD-PV;and(3)Congenital cardiovascular malformations.Outcomes:Recommendation for liver transplantation.Lessons:The choice of treatment options for neonatal biliary atresia combined with PD-PV.
基金
The Science Foundation of Suzhou Science and Technology Bureau,No.SYS201758 and No.SYS2020158
and Youth Science and technology project of revitalizing health by science and education in Suzhou in 2019,No.KJXW2019020.