肺动脉闭锁伴室间隔缺损的外科手术策略进展

Progress in surgical strategies of pulmonary atresia with ventricular septal defect

肺动脉闭锁伴室间隔缺损是最为常见的复杂右心畸形之一。大型主肺侧支动脉的存在及肺血管发育个体差异化明显,使得该畸形的解剖分型及外科手术方式多样,治疗效果不甚理想。目前,国内外尚缺乏针对单源化手术和分期手术等治疗策略的统一标准和流程。该文就肺动脉闭锁伴室间隔缺损的外科诊治及手术策略进展进行综述。

Pulmonary atresia with ventricular septal defect is one of the most common complex right heart malformations.The existence of major aortopulmonary collateral arteries and the individual differences in pulmonary vascular development make the anatomical classification and surgical methods of this disease variable,and the treatment effect is not ideal.At present,there is still a lack of unified standards and procedures for treatment strategies such as unifocalization and staged surgery at home and abroad.This article reviews the progress of surgical diagnosis and treatment and surgical strategy of pulmonary atresia with ventricular septal defect.