Selection of surgical strategies for vulvar Paget’s disease

Extramammary Paget disease(EMPD)is an uncommon intraepithelial adenocarcinoma that tends to occur in regions with an abundance of apocrine glands.EMPD typically affects older individuals aged 50 to 80 years.The most commonly affected area of EMPD is the vulva;it accounts for 1%to 2%of vulvar malignancies.[1]The most common symptoms are chronic itching,vulvar pain,and erythema.However,symptoms can vary,and patients can remain asymptomatic for years.The typical feature of vulvar Paget’s disease(VPD)is an"icing cake effect"on the skin.[2]This disease is often misdiagnosed as eczema.Treatment delay is usually more than 2 years,and treatment can sometimes result in failure with a high recurrence rate.