经皮肺动脉球囊成形术治疗原发性血小板增多症相关慢性血栓栓塞性肺高血压一例

A case report of percutaneous transluminal pulmonary angioplasty applied to chronic thromboembolic pulmonary hypertension associated with essential thrombocythemia

原发性血小板增多症相关慢性血栓栓塞性肺高血压的病例罕见,治疗策略尚缺乏共识。该文报道一例69岁女性,因反复活动后气短入院,诊断为慢性血栓栓塞性肺高血压、原发性血小板增多症,综合运用经皮肺动脉球囊成形术、血小板单采术、羟基脲、抗凝及抗血小板等治疗后患者临床症状明显缓解。此病例提示,原发性血小板增多症相关慢性血栓栓塞性肺高血压在常规介入及抗凝治疗的基础上,需充分考虑针对病因的治疗以获得最佳临床效果。