摘要
一、概述获得性血友病A(Acquired Hemophilia A,AHA)是一种由于循环血中出现抗凝血因子Ⅷ(FⅧ)自身抗体导致FⅧ活性(FⅧ∶C)降低的获得性出血性疾病。其特点为既往无出血史和无阳性家族史的患者出现自发性出血或者在手术、外伤或侵入性检查时发生异常出血。出凝血筛查以孤立性活化的部分凝血活酶时间(APTT)延长为特征。
作者
中华医学会血液学分会血栓与止血学组
中国血友病协作组
杨仁池
Thrombosis and Hemostasis Group,Chinese Society of Hematology,Chinese Medical Association;Hemophilia Treatment Center Collaborative Network of China;Yang Renchi(不详;State Key Laboratory of Experimental Hematology,National Clinical Research Center for Blood Diseases,Institute of Hematology and Blood Diseases Hospital,Chinese Academy of Medical Sciences and Peking Union Medical College,Tianjin 300020,China)
出处
《中华血液学杂志》
CAS
CSCD
北大核心
2021年第10期793-799,共7页
Chinese Journal of Hematology