摘要
1内耳畸形定义及分类先天性内耳畸形为胚胎期不同阶段内耳发育障碍导致内耳异常的一组疾病,发病率为1/2000~1/6000[1]。内耳畸形分为骨迷路畸形和膜迷路畸形。骨迷路在胚胎第4周和第8周之间发育,从第8周开始骨化,在此期间形成的结构性畸形可以通过影像学检查来诊断,而膜迷路畸形无法通过常规的影像学检查诊断[2]。在单侧先天性感音神经性聋患者中,66.7%伴有内耳和(或)内听道畸形[3]。
Cerebrospinal fluid otorrhea caused by inner ear malformation is rare, and its clinical manifestations are atypical. Therefore, it can easy be misdiagnosed or missed. Recurrent meningitis caused by inner ear malformation can lead to serious complications. This article reviews the classification of inner ear malformation, the etiology the common fistula locations, clinical features, imaging features, surgical approaches, postoperative complications and influencing factors of surgical efficacy of cerebrospinal fluid otorrhea due to inner ear malformation.
作者
吴宏
蔡鑫章
WU Hong;CAI Xinzhang
出处
《临床耳鼻咽喉头颈外科杂志》
CSCD
北大核心
2021年第11期1048-1052,共5页
Journal of Clinical Otorhinolaryngology Head And Neck Surgery
基金
长沙市自然科学基金资助项目(No:kq2014291)
湖南省自然科学基金(No:2017JJ3476)。
关键词
内耳畸形
脑脊液耳漏
镫骨
外科手术
inner ear malformation
cerebrospinal fluid otorrhea
stapes
surgical procedures
operative
